Orbital lymphatic-venous malformation with concomitant spontaneous orbital arteriovenous fistula: Case report

• Main Authors: Bunyada Putthirangsiwong, Dinesh Selva, Weerawan Chokthaweesak, Ekachat Chanthanaphak, Sirintara Singhara Na Ayudhaya
• Other Authors: Faculty of Medicine, Ramathibodi Hospital, Mahidol University
• Format: Review
• Published: 2019
• Subjects: Medicine
• Online Access: https://repository.li.mahidol.ac.th/handle/123456789/46967
• Institution: Mahidol University

The authors describe the case of an 11-year-old boy with no history of prior trauma, who experienced acute proptosis and visual loss while showering. Diagnostic carotid artery angiography revealed an orbital lymphatic-venous malformation (LVM) concomitant with an intraorbital arteriovenous fistula. The patient was treated with transvenous coil and N-butyl cyanoacrylate glue embolization, combined with direct percutaneous glue injection into the LVM followed by excision. There was good clinical and radiological response without recurrence at the 2-year follow-up. Diagnostic carotid angiography should be considered in cases of orbital LVM, as a concomitant arteriovenous fistula might be present in rare cases.