Hemispherectomy procedure in proteus syndrome
Proteus syndrome is a rare overgrowth disorder including bone, soft tissue, and skin. Central nervous system manifestations were reported in about 40% of the patients including hemimegalencephaly and the resultant hemicranial hyperplasia, convulsions and mental deficiency. We report a 1-month-old ma...
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The Iranian Child Neurology Society
2016
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Online Access: | http://repository.unair.ac.id/100045/1/15.%20Hemispherectomy%20in%20proteus%20Iran%20J%20Child%20Neurol.pdf http://repository.unair.ac.id/100045/2/Hemispherectomy%20procedure.pdf http://repository.unair.ac.id/100045/3/Hemispherectomy%20in%20procedure%20in%20proteus%20syndrome.pdf http://repository.unair.ac.id/100045/ https://journals.sbmu.ac.ir/ijcn/article/view/9797 https://doi.org/10.22037/ijcn.v10i3.9797 |
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id-langga.1000452020-10-16T07:16:29Z http://repository.unair.ac.id/100045/ Hemispherectomy procedure in proteus syndrome Prastiya Indra Gunawan Lusiana Darto Saharso R Medicine (General) RJ Pediatrics Proteus syndrome is a rare overgrowth disorder including bone, soft tissue, and skin. Central nervous system manifestations were reported in about 40% of the patients including hemimegalencephaly and the resultant hemicranial hyperplasia, convulsions and mental deficiency. We report a 1-month-old male baby referred to Pediatric Neurology Clinic Soetomo Hospital, Surabaya, Indonesia in 2014 presented recurrent seizures since birth with asymmetric dysmorphic face with the right side larger than the left, subcutaneous mass and linear nevi. Craniocervical MRI revealed hemimegalencephaly right cerebral hemisphere. Triple antiepileptic drugs were already given as well as the ketogenic diet, but the seizures persisted. The seizure then was resolved after hemispherectomy procedure. The Iranian Child Neurology Society 2016 Article PeerReviewed text en http://repository.unair.ac.id/100045/1/15.%20Hemispherectomy%20in%20proteus%20Iran%20J%20Child%20Neurol.pdf text en http://repository.unair.ac.id/100045/2/Hemispherectomy%20procedure.pdf text en http://repository.unair.ac.id/100045/3/Hemispherectomy%20in%20procedure%20in%20proteus%20syndrome.pdf Prastiya Indra Gunawan and Lusiana and Darto Saharso (2016) Hemispherectomy procedure in proteus syndrome. Iranian Journal of Child Neurology, 10 (3). pp. 86-90. ISSN 20080700 https://journals.sbmu.ac.ir/ijcn/article/view/9797 https://doi.org/10.22037/ijcn.v10i3.9797 |
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R Medicine (General) RJ Pediatrics Prastiya Indra Gunawan Lusiana Darto Saharso Hemispherectomy procedure in proteus syndrome |
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Proteus syndrome is a rare overgrowth disorder including bone, soft tissue, and skin. Central nervous system manifestations were reported in about 40% of the patients including hemimegalencephaly and the resultant hemicranial hyperplasia, convulsions and mental deficiency. We report a 1-month-old male baby referred to Pediatric Neurology Clinic Soetomo Hospital, Surabaya, Indonesia in 2014 presented recurrent seizures since birth with asymmetric dysmorphic face with the right side larger than the left, subcutaneous mass and linear nevi. Craniocervical MRI revealed hemimegalencephaly right cerebral hemisphere. Triple antiepileptic drugs were already given as well as the ketogenic diet, but the seizures persisted. The seizure then was resolved after hemispherectomy procedure. |
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Article PeerReviewed |
author |
Prastiya Indra Gunawan Lusiana Darto Saharso |
author_facet |
Prastiya Indra Gunawan Lusiana Darto Saharso |
author_sort |
Prastiya Indra Gunawan |
title |
Hemispherectomy procedure in proteus syndrome |
title_short |
Hemispherectomy procedure in proteus syndrome |
title_full |
Hemispherectomy procedure in proteus syndrome |
title_fullStr |
Hemispherectomy procedure in proteus syndrome |
title_full_unstemmed |
Hemispherectomy procedure in proteus syndrome |
title_sort |
hemispherectomy procedure in proteus syndrome |
publisher |
The Iranian Child Neurology Society |
publishDate |
2016 |
url |
http://repository.unair.ac.id/100045/1/15.%20Hemispherectomy%20in%20proteus%20Iran%20J%20Child%20Neurol.pdf http://repository.unair.ac.id/100045/2/Hemispherectomy%20procedure.pdf http://repository.unair.ac.id/100045/3/Hemispherectomy%20in%20procedure%20in%20proteus%20syndrome.pdf http://repository.unair.ac.id/100045/ https://journals.sbmu.ac.ir/ijcn/article/view/9797 https://doi.org/10.22037/ijcn.v10i3.9797 |
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