Osteogenesis Imperfecta: An Overview
Osteogenesis Imperfecta (OI) or commonly referred to as brittle bone disease is a congenital connective tissue formation disorder characterized by bone fragility, osteopenia, skin disorders, blue sclera, dentinogenesis imperfecta (DI), and hearing loss. The diagnosis of Osteogenesis Imperfecta is ba...
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International Journal of Scientific Advances (IJSCIA)
2022
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id-langga.1275892023-06-25T11:19:41Z https://repository.unair.ac.id/127589/ Osteogenesis Imperfecta: An Overview Rahma Ira Mustikasari, - Nur Rochmah, - Muhammad Faizi, - Qurrota Ayuni Novia Putri, - R Medicine (General) RJ Pediatrics Osteogenesis Imperfecta (OI) or commonly referred to as brittle bone disease is a congenital connective tissue formation disorder characterized by bone fragility, osteopenia, skin disorders, blue sclera, dentinogenesis imperfecta (DI), and hearing loss. The diagnosis of Osteogenesis Imperfecta is based on history, clinical examination, lumbar bone density, bone biochemistry and radiographic findings. Diagnosis of osteogenesis imperfecta can be difficult and some primary skeletal disorders can be mixed with osteogenesis imperfecta. Management of OI requires a multidisciplinary approach such as endocrinologists, pediatricians, orthopedic surgeons, dentists, medical rehabilitation specialists, geneticists, psychologists, and occupational therapists. Bisphosphonate therapy has been shown to be effective in reducing pain, fracture frequency, and disability. Medical services such as bisphosphonate treatment and rehabilitation in individuals with OI have the long-term goal of optimizing the health and well-being of bone fragility and deformity. International Journal of Scientific Advances (IJSCIA) 2022 Article PeerReviewed text en https://repository.unair.ac.id/127589/3/31%20-%20Artikel.pdf text en https://repository.unair.ac.id/127589/1/31%20-%20Kualitas%20Karil.pdf text en https://repository.unair.ac.id/127589/2/31%20-%20Turnitin.pdf text en https://repository.unair.ac.id/127589/7/Karil%20-%20Osteogenesis%20Imperfecta%20An%20Overview.pdf Rahma Ira Mustikasari, - and Nur Rochmah, - and Muhammad Faizi, - and Qurrota Ayuni Novia Putri, - (2022) Osteogenesis Imperfecta: An Overview. International Journal of Scientific Advances, 3 (3). pp. 351-357. ISSN 2708-7972 https://www.ijscia.com/?p=9572 |
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R Medicine (General) RJ Pediatrics Rahma Ira Mustikasari, - Nur Rochmah, - Muhammad Faizi, - Qurrota Ayuni Novia Putri, - Osteogenesis Imperfecta: An Overview |
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Osteogenesis Imperfecta (OI) or commonly referred to as brittle bone disease is a congenital connective tissue formation disorder characterized by bone fragility, osteopenia, skin disorders, blue sclera, dentinogenesis imperfecta (DI), and hearing loss. The diagnosis of Osteogenesis Imperfecta is based on history, clinical examination, lumbar bone density, bone biochemistry and radiographic findings. Diagnosis of osteogenesis imperfecta can be difficult and some primary skeletal disorders can be mixed with osteogenesis imperfecta. Management of OI requires a multidisciplinary approach such as endocrinologists, pediatricians, orthopedic surgeons, dentists, medical rehabilitation specialists, geneticists, psychologists, and occupational therapists. Bisphosphonate therapy has been shown to be effective in reducing pain, fracture frequency, and disability. Medical services such as bisphosphonate treatment and rehabilitation in individuals with OI have the long-term goal of optimizing the health and well-being of bone fragility and deformity. |
format |
Article PeerReviewed |
author |
Rahma Ira Mustikasari, - Nur Rochmah, - Muhammad Faizi, - Qurrota Ayuni Novia Putri, - |
author_facet |
Rahma Ira Mustikasari, - Nur Rochmah, - Muhammad Faizi, - Qurrota Ayuni Novia Putri, - |
author_sort |
Rahma Ira Mustikasari, - |
title |
Osteogenesis Imperfecta: An Overview |
title_short |
Osteogenesis Imperfecta: An Overview |
title_full |
Osteogenesis Imperfecta: An Overview |
title_fullStr |
Osteogenesis Imperfecta: An Overview |
title_full_unstemmed |
Osteogenesis Imperfecta: An Overview |
title_sort |
osteogenesis imperfecta: an overview |
publisher |
International Journal of Scientific Advances (IJSCIA) |
publishDate |
2022 |
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https://repository.unair.ac.id/127589/3/31%20-%20Artikel.pdf https://repository.unair.ac.id/127589/1/31%20-%20Kualitas%20Karil.pdf https://repository.unair.ac.id/127589/2/31%20-%20Turnitin.pdf https://repository.unair.ac.id/127589/7/Karil%20-%20Osteogenesis%20Imperfecta%20An%20Overview.pdf https://repository.unair.ac.id/127589/ https://www.ijscia.com/?p=9572 |
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