Single-stage open repair of severe asymmetric pectus excavatum and mitral valve replacement in connective tissue disease

Single-stage open repair of severe asymmetric pectus excavatum and mitral valve replacement in connective tissue disease

We present a 14-year-old boy with Loey–Dietz syndrome with severe mitral regurgitation, pectus excavatum and scoliosis. The Haller index was 25. The heart was displaced into the left hemithorax. The right inferior pulmonary vein was very close to the sternum and vertebral body. Single-stage surgery...

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Main Authors: Pau, Cheong Ping, Chong, Kee Soon, Yakub, Mohd Azhari, Abdul Khalil, Alizan
Format: Article
Published: SAGE Publications Inc. 2022
Subjects:
RD Surgery
Online Access:http://eprints.um.edu.my/43504/
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Institution: Universiti Malaya
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spelling my.um.eprints.435042023-10-23T03:59:59Z http://eprints.um.edu.my/43504/ Single-stage open repair of severe asymmetric pectus excavatum and mitral valve replacement in connective tissue disease Pau, Cheong Ping Chong, Kee Soon Yakub, Mohd Azhari Abdul Khalil, Alizan RD Surgery We present a 14-year-old boy with Loey–Dietz syndrome with severe mitral regurgitation, pectus excavatum and scoliosis. The Haller index was 25. The heart was displaced into the left hemithorax. The right inferior pulmonary vein was very close to the sternum and vertebral body. Single-stage surgery was performed. An osseo-myo-cutaneous pedicled flap was created by sterno-manubrial junction dislocation and rib resection with bilateral internal mammary arteries supplying the flap. Cardiopulmonary bypass and mitral valve replacement was performed. The defect was bridged with three straight plates. The flap was laid on top and anchored. Early outcome at three months was good. © The Author(s) 2021. SAGE Publications Inc. 2022-05 Article PeerReviewed Pau, Cheong Ping and Chong, Kee Soon and Yakub, Mohd Azhari and Abdul Khalil, Alizan (2022) Single-stage open repair of severe asymmetric pectus excavatum and mitral valve replacement in connective tissue disease. Asian Cardiovascular and Thoracic Annals, 30 (4). 480 – 482. ISSN 0218-4923, DOI https://doi.org/10.1177/02184923211014004 <https://doi.org/10.1177/02184923211014004>. 10.1177/02184923211014004
institution Universiti Malaya
building UM Library
collection Institutional Repository
continent Asia
country Malaysia
content_provider Universiti Malaya
content_source UM Research Repository
url_provider http://eprints.um.edu.my/
topic RD Surgery
spellingShingle RD Surgery
Pau, Cheong Ping
Chong, Kee Soon
Yakub, Mohd Azhari
Abdul Khalil, Alizan
Single-stage open repair of severe asymmetric pectus excavatum and mitral valve replacement in connective tissue disease
description We present a 14-year-old boy with Loey–Dietz syndrome with severe mitral regurgitation, pectus excavatum and scoliosis. The Haller index was 25. The heart was displaced into the left hemithorax. The right inferior pulmonary vein was very close to the sternum and vertebral body. Single-stage surgery was performed. An osseo-myo-cutaneous pedicled flap was created by sterno-manubrial junction dislocation and rib resection with bilateral internal mammary arteries supplying the flap. Cardiopulmonary bypass and mitral valve replacement was performed. The defect was bridged with three straight plates. The flap was laid on top and anchored. Early outcome at three months was good. © The Author(s) 2021.
format Article
author Pau, Cheong Ping
Chong, Kee Soon
Yakub, Mohd Azhari
Abdul Khalil, Alizan
author_facet Pau, Cheong Ping
Chong, Kee Soon
Yakub, Mohd Azhari
Abdul Khalil, Alizan
author_sort Pau, Cheong Ping
title Single-stage open repair of severe asymmetric pectus excavatum and mitral valve replacement in connective tissue disease
title_short Single-stage open repair of severe asymmetric pectus excavatum and mitral valve replacement in connective tissue disease
title_full Single-stage open repair of severe asymmetric pectus excavatum and mitral valve replacement in connective tissue disease
title_fullStr Single-stage open repair of severe asymmetric pectus excavatum and mitral valve replacement in connective tissue disease
title_full_unstemmed Single-stage open repair of severe asymmetric pectus excavatum and mitral valve replacement in connective tissue disease
title_sort single-stage open repair of severe asymmetric pectus excavatum and mitral valve replacement in connective tissue disease
publisher SAGE Publications Inc.
publishDate 2022
url http://eprints.um.edu.my/43504/
_version_ 1781704676398333952

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