Unilateral pulmonary vein atresia presenting with recurrent haemoptysis in a child : a case report
Background: Haemoptysis is an uncommon presenting symptom in children and is usually caused by acute lower respiratory tract infection or foreign body aspiration. We report a rare case of right unilateral pulmonary vein atresia (PVA) as the underlying aetiology of recurrent haemoptysis in a child....
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| Main Authors: | , , , , , , , , |
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| Format: | Article |
| Language: | English |
| Published: |
BioMed Central Ltd.
2021
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| Subjects: | |
| Online Access: | http://ir.unimas.my/id/eprint/45262/1/Unilateral%20pulmonary.pdf http://ir.unimas.my/id/eprint/45262/ https://bmcpediatr.biomedcentral.com/articles/10.1186/s12887-020-02348-7 https://doi.org/10.1186/s12887-020-02348-7 |
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| Institution: | Universiti Malaysia Sarawak |
| Language: | English |
| Summary: | Background: Haemoptysis is an uncommon presenting symptom in children and is usually caused by acute lower respiratory tract infection or foreign body aspiration. We report a rare case of right unilateral pulmonary vein atresia (PVA) as the underlying aetiology of recurrent haemoptysis in a child.
Case presentation: A 4 years old girl presented with history of recurrent haemoptysis. Bronchoscopic evaluation
excluded a foreign body aspiration but revealed right bronchial mucosal hyperaemia and varices. Diagnosis of right
unilateral PVA was suspected on transthoracic echocardiography which demonstrated hypoplastic right pulmonary artery and non-visualization of right pulmonary veins. Final diagnosis was confirmed on cardiac CT angiography. A conservative treatment approach was opted with consideration for pneumonectomy in future when she is older.
Conclusion: Rarer causes should be considered when investigating for recurrent haemoptysis in children.
Bronchoscopy and cardiac imaging are useful tools to establish the diagnosis of unilateral PVA in our case. |
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