Sonographic features of Ebstein anomaly associated with hydrops fetalis: A report of two cases

Ebstein anomaly, an abnormally low insertion of the tricuspid valve, occurs in 0.5% of patients with congenital heart disease. In rare cases, this disorder may be complicated by congestive heart failure in utero and hydrops fetalis. This article reports the prenatal sonographic features of 2 cases o...

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Main Authors: Tongsong T., Chanprapaph P., Khunamornpong S., Sirichotiyakul S.
Format: Article
Language:English
Published: 2014
Online Access:http://www.scopus.com/inward/record.url?eid=2-s2.0-15044345182&partnerID=40&md5=331ddfde81048e7f3b3223b83efd8c6b
http://www.ncbi.nlm.nih.gov/pubmed/15756659
http://cmuir.cmu.ac.th/handle/6653943832/1938
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Institution: Chiang Mai University
Language: English
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spelling th-cmuir.6653943832-19382014-08-30T02:00:17Z Sonographic features of Ebstein anomaly associated with hydrops fetalis: A report of two cases Tongsong T. Chanprapaph P. Khunamornpong S. Sirichotiyakul S. Ebstein anomaly, an abnormally low insertion of the tricuspid valve, occurs in 0.5% of patients with congenital heart disease. In rare cases, this disorder may be complicated by congestive heart failure in utero and hydrops fetalis. This article reports the prenatal sonographic features of 2 cases of Ebstein anomaly associated with hydrops fetalis. In both cases, fetal echocardiography was performed at 34 weeks of gestation. The 4-chamber view showed fetal cardiomegaly and pericardial effusion. In both cases, the annular attachment of the tricuspid valve leaflets was difficult to demonstrate and so distal that it could easily be confused with papillary muscle in the right ventricular wall. Poor fetal cardiac hemodynamics with severe tricuspid regurgitation was demonstrated by pulsed Doppler imaging. Pulmonary regurgitation was also clearly demonstrated in both cases. Preterm delivery with stillbirth occurred in both cases. Autopsies confirmed the very distal displacement of the tricuspid valve insertion, close to the apex, and enlargement of the right atrium. © 2005 Wiley Periodicals, Inc. 2014-08-30T02:00:17Z 2014-08-30T02:00:17Z 2005 Article 00912751 10.1002/jcu.20102 15756659 JCULD http://www.scopus.com/inward/record.url?eid=2-s2.0-15044345182&partnerID=40&md5=331ddfde81048e7f3b3223b83efd8c6b http://www.ncbi.nlm.nih.gov/pubmed/15756659 http://cmuir.cmu.ac.th/handle/6653943832/1938 English
institution Chiang Mai University
building Chiang Mai University Library
country Thailand
collection CMU Intellectual Repository
language English
description Ebstein anomaly, an abnormally low insertion of the tricuspid valve, occurs in 0.5% of patients with congenital heart disease. In rare cases, this disorder may be complicated by congestive heart failure in utero and hydrops fetalis. This article reports the prenatal sonographic features of 2 cases of Ebstein anomaly associated with hydrops fetalis. In both cases, fetal echocardiography was performed at 34 weeks of gestation. The 4-chamber view showed fetal cardiomegaly and pericardial effusion. In both cases, the annular attachment of the tricuspid valve leaflets was difficult to demonstrate and so distal that it could easily be confused with papillary muscle in the right ventricular wall. Poor fetal cardiac hemodynamics with severe tricuspid regurgitation was demonstrated by pulsed Doppler imaging. Pulmonary regurgitation was also clearly demonstrated in both cases. Preterm delivery with stillbirth occurred in both cases. Autopsies confirmed the very distal displacement of the tricuspid valve insertion, close to the apex, and enlargement of the right atrium. © 2005 Wiley Periodicals, Inc.
format Article
author Tongsong T.
Chanprapaph P.
Khunamornpong S.
Sirichotiyakul S.
spellingShingle Tongsong T.
Chanprapaph P.
Khunamornpong S.
Sirichotiyakul S.
Sonographic features of Ebstein anomaly associated with hydrops fetalis: A report of two cases
author_facet Tongsong T.
Chanprapaph P.
Khunamornpong S.
Sirichotiyakul S.
author_sort Tongsong T.
title Sonographic features of Ebstein anomaly associated with hydrops fetalis: A report of two cases
title_short Sonographic features of Ebstein anomaly associated with hydrops fetalis: A report of two cases
title_full Sonographic features of Ebstein anomaly associated with hydrops fetalis: A report of two cases
title_fullStr Sonographic features of Ebstein anomaly associated with hydrops fetalis: A report of two cases
title_full_unstemmed Sonographic features of Ebstein anomaly associated with hydrops fetalis: A report of two cases
title_sort sonographic features of ebstein anomaly associated with hydrops fetalis: a report of two cases
publishDate 2014
url http://www.scopus.com/inward/record.url?eid=2-s2.0-15044345182&partnerID=40&md5=331ddfde81048e7f3b3223b83efd8c6b
http://www.ncbi.nlm.nih.gov/pubmed/15756659
http://cmuir.cmu.ac.th/handle/6653943832/1938
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