Case report: Persistent hyperinsulinemic hypoglycemia of infancy associated with congenital neuroblastoma: A case report
The authors report a rare case of persistent hyperinsulinemic hypoglycemia of infancy (PHHI) with congenital neuroblastoma without feature(s) of Beckwith-Wiedemann syndrome. A term newborn with a birth weight of 3,900g developed hypoglycemia one hour after birth and required up to 20 mg/kg/min of in...
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th-cmuir.6653943832-510612018-09-04T04:50:58Z Case report: Persistent hyperinsulinemic hypoglycemia of infancy associated with congenital neuroblastoma: A case report Prapai Dejkhamron Kevalee Unachak Pattra Thanarattanakorn Pimlak D. Charoenkwan Watcharee Tantiprabha Somporn Chotinaruemol Benjaporn Chaiwun MD Medicine The authors report a rare case of persistent hyperinsulinemic hypoglycemia of infancy (PHHI) with congenital neuroblastoma without feature(s) of Beckwith-Wiedemann syndrome. A term newborn with a birth weight of 3,900g developed hypoglycemia one hour after birth and required up to 20 mg/kg/min of intravenous glucose infusion to maintain euglycemia. Investigations during the critical period revealed an inappropriately high insulin level. An abdominal CT scan revealed a normal pancreas, right suprarenal mass, and liver nodules. A condition of stage 4S neuroblastoma was suspected and supported by an increased ratio of urine vanillylmandelic acid to creatinine. The bone marrow smear was normal. She underwent near total pancreatectomy at the age of 2 months. The suprarenal mass and liver nodules were not found during the operation or during repeated abdominal CT scans at 3 month of age. Spontaneous regression of neuroblastoma was suspected. The pathology of the pancreas was compatible with PHHI. 2018-09-04T04:50:58Z 2018-09-04T04:50:58Z 2010-06-01 Journal 01252208 01252208 2-s2.0-77954481356 https://www.scopus.com/inward/record.uri?partnerID=HzOxMe3b&scp=77954481356&origin=inward http://cmuir.cmu.ac.th/jspui/handle/6653943832/51061 |
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Medicine Prapai Dejkhamron Kevalee Unachak Pattra Thanarattanakorn Pimlak D. Charoenkwan Watcharee Tantiprabha Somporn Chotinaruemol Benjaporn Chaiwun MD Case report: Persistent hyperinsulinemic hypoglycemia of infancy associated with congenital neuroblastoma: A case report |
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The authors report a rare case of persistent hyperinsulinemic hypoglycemia of infancy (PHHI) with congenital neuroblastoma without feature(s) of Beckwith-Wiedemann syndrome. A term newborn with a birth weight of 3,900g developed hypoglycemia one hour after birth and required up to 20 mg/kg/min of intravenous glucose infusion to maintain euglycemia. Investigations during the critical period revealed an inappropriately high insulin level. An abdominal CT scan revealed a normal pancreas, right suprarenal mass, and liver nodules. A condition of stage 4S neuroblastoma was suspected and supported by an increased ratio of urine vanillylmandelic acid to creatinine. The bone marrow smear was normal. She underwent near total pancreatectomy at the age of 2 months. The suprarenal mass and liver nodules were not found during the operation or during repeated abdominal CT scans at 3 month of age. Spontaneous regression of neuroblastoma was suspected. The pathology of the pancreas was compatible with PHHI. |
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Journal |
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Prapai Dejkhamron Kevalee Unachak Pattra Thanarattanakorn Pimlak D. Charoenkwan Watcharee Tantiprabha Somporn Chotinaruemol Benjaporn Chaiwun MD |
author_facet |
Prapai Dejkhamron Kevalee Unachak Pattra Thanarattanakorn Pimlak D. Charoenkwan Watcharee Tantiprabha Somporn Chotinaruemol Benjaporn Chaiwun MD |
author_sort |
Prapai Dejkhamron |
title |
Case report: Persistent hyperinsulinemic hypoglycemia of infancy associated with congenital neuroblastoma: A case report |
title_short |
Case report: Persistent hyperinsulinemic hypoglycemia of infancy associated with congenital neuroblastoma: A case report |
title_full |
Case report: Persistent hyperinsulinemic hypoglycemia of infancy associated with congenital neuroblastoma: A case report |
title_fullStr |
Case report: Persistent hyperinsulinemic hypoglycemia of infancy associated with congenital neuroblastoma: A case report |
title_full_unstemmed |
Case report: Persistent hyperinsulinemic hypoglycemia of infancy associated with congenital neuroblastoma: A case report |
title_sort |
case report: persistent hyperinsulinemic hypoglycemia of infancy associated with congenital neuroblastoma: a case report |
publishDate |
2018 |
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https://www.scopus.com/inward/record.uri?partnerID=HzOxMe3b&scp=77954481356&origin=inward http://cmuir.cmu.ac.th/jspui/handle/6653943832/51061 |
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