Giant choledochal cyst and infantile polycystic kidneys as prenatal sonographic features of Caroli syndrome

Giant choledochal cyst and infantile polycystic kidneys as prenatal sonographic features of Caroli syndrome

© 2019 Wiley Periodicals, Inc. Caroli syndrome is a developmental disorder caused by complete or partial arrest of ductal plate remodeling, leading to dilated bile ducts along with fibrosis surrounding the portal tracts. It is most commonly associated with autosomal recessive polycystic kidney (ARPK...

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Main Authors: Kuntharee Traisrisilp, Fuanglada Tongprasert, Komson Wannasai, Theera Tongsong
Format: Journal
Published: 2020
Subjects:
Medicine
Online Access:https://www.scopus.com/inward/record.uri?partnerID=HzOxMe3b&scp=85073977450&origin=inward
http://cmuir.cmu.ac.th/jspui/handle/6653943832/68520
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Institution: Chiang Mai University
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spelling th-cmuir.6653943832-685202020-04-02T15:28:42Z Giant choledochal cyst and infantile polycystic kidneys as prenatal sonographic features of Caroli syndrome Kuntharee Traisrisilp Fuanglada Tongprasert Komson Wannasai Theera Tongsong Medicine © 2019 Wiley Periodicals, Inc. Caroli syndrome is a developmental disorder caused by complete or partial arrest of ductal plate remodeling, leading to dilated bile ducts along with fibrosis surrounding the portal tracts. It is most commonly associated with autosomal recessive polycystic kidney (ARPKD). We report a unique case of Caroli syndrome, diagnosed prenatally at 24 weeks of gestation in a 29-year-old Thai woman. Ultrasound findings revealed the association of a fetal giant choledochal cyst with ARPKD. Autopsy findings showed ductal plate malformation, typical of Caroli syndrome, associated with giant choledocal cyst and ARPKD. 2020-04-02T15:28:42Z 2020-04-02T15:28:42Z 2020-01-01 Journal 10970096 00912751 2-s2.0-85073977450 10.1002/jcu.22778 https://www.scopus.com/inward/record.uri?partnerID=HzOxMe3b&scp=85073977450&origin=inward http://cmuir.cmu.ac.th/jspui/handle/6653943832/68520
institution Chiang Mai University
building Chiang Mai University Library
country Thailand
collection CMU Intellectual Repository
topic Medicine
spellingShingle Medicine
Kuntharee Traisrisilp
Fuanglada Tongprasert
Komson Wannasai
Theera Tongsong
Giant choledochal cyst and infantile polycystic kidneys as prenatal sonographic features of Caroli syndrome
description © 2019 Wiley Periodicals, Inc. Caroli syndrome is a developmental disorder caused by complete or partial arrest of ductal plate remodeling, leading to dilated bile ducts along with fibrosis surrounding the portal tracts. It is most commonly associated with autosomal recessive polycystic kidney (ARPKD). We report a unique case of Caroli syndrome, diagnosed prenatally at 24 weeks of gestation in a 29-year-old Thai woman. Ultrasound findings revealed the association of a fetal giant choledochal cyst with ARPKD. Autopsy findings showed ductal plate malformation, typical of Caroli syndrome, associated with giant choledocal cyst and ARPKD.
format Journal
author Kuntharee Traisrisilp
Fuanglada Tongprasert
Komson Wannasai
Theera Tongsong
author_facet Kuntharee Traisrisilp
Fuanglada Tongprasert
Komson Wannasai
Theera Tongsong
author_sort Kuntharee Traisrisilp
title Giant choledochal cyst and infantile polycystic kidneys as prenatal sonographic features of Caroli syndrome
title_short Giant choledochal cyst and infantile polycystic kidneys as prenatal sonographic features of Caroli syndrome
title_full Giant choledochal cyst and infantile polycystic kidneys as prenatal sonographic features of Caroli syndrome
title_fullStr Giant choledochal cyst and infantile polycystic kidneys as prenatal sonographic features of Caroli syndrome
title_full_unstemmed Giant choledochal cyst and infantile polycystic kidneys as prenatal sonographic features of Caroli syndrome
title_sort giant choledochal cyst and infantile polycystic kidneys as prenatal sonographic features of caroli syndrome
publishDate 2020
url https://www.scopus.com/inward/record.uri?partnerID=HzOxMe3b&scp=85073977450&origin=inward
http://cmuir.cmu.ac.th/jspui/handle/6653943832/68520
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