Activation of Endoplasmic Reticulum Stress and Unfolded Protein Response in Congenital Factor VII Deficiency
© 2018 Schattauer. Congenital factor (F) VII deficiency is a bleeding disorder caused by a heterogeneous pattern of mutations in the F7 gene. Protein misfolding due to mutations is a strong candidate mechanism to produce the highly represented type I FVII deficiency forms, characterized by a concomi...
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Main Authors: | Elisabeth Andersen, Maria Eugenia Chollet, Christiane Filion Myklebust, Mirko Pinotti, Francesco Bernardi, Ampaiwan Chuansumrit, Ellen Skarpen, Per Morten Sandset, Grethe Skretting |
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Other Authors: | Oslo University Hospital |
Format: | Article |
Published: |
2019
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Subjects: | |
Online Access: | https://repository.li.mahidol.ac.th/handle/123456789/46803 |
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Institution: | Mahidol University |
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